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Disease definition

Chorea-acanthocytosis (ChAc) is a form of neuroacanthocytosis (see this term) and is characterized clinically by a Huntington disease-like phenotype with progressive neurological symptoms including movement disorders, psychiatric manifestations and cognitive disturbances.


  • Synonym(s):
    • ChAc
    • Chorea-acanthocytosis
    • Levine-Critchley syndrome
  • Prevalence: Unknown
  • Inheritance: Autosomal recessive 
  • Age of onset: Adult
  • ICD-10: E78.6
  • OMIM: 200150
  • UMLS: C0393576
  • MeSH: -
  • GARD: 3956
  • MedDRA: -

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