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Classic progressive supranuclear palsy syndrome

Disease definition

A classical form of progressive supranuclear palsy (PSP), a rare late-onset neurodegenerative disease, characterized by slowing of vertical saccadic eye movements, falls due to postural instability, axial akinetic-rigid syndrome, and cognitive impairment. Difficulties in speech and swallowing may develop.


Classification level: Subtype of disorder
  • Synonym(s):
    • Classic PSP syndrome
    • Richardson syndrome
    • Steele-Richardson-Olszewski disease
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: G23.1
  • ICD-11: 8A00.10
  • OMIM: 601104  609454  610898
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


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