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Actinic lichen planus
Disease definition
A rare cutaneous lichen planus characterized by the development of photo-distributed lichenoid lesions.
ORPHA:254395
Classification level: Disorder- Synonym(s):
- Actinic LP
- Lichen planus actinus
- Lichen planus subtropicus
- Lichen planus tropicus
- Lichenoid melanodermatitis
- Summertime actinic lichenoid eruption
- Prevalence: Unknown
- Inheritance: -
- Age of onset: All ages
- ICD-10: L43.8
- OMIM: -
- UMLS: C0406365
- MeSH: -
- GARD: 12673
- MedDRA: -
Summary
Epidemiology
The exact prevalence is unknown. It is extremely rare in Caucasians but it is more common in dark-skinned populations, particularly in young adults.
Clinical description
Indurated plaques or papules erupt on the face, neck, and the dorsal surface of hands after exposure to ultraviolet (UV) light. Different morphological subtypes have been described: the classic form (violaceous papules), a granuloma annular-like form (annular erythematous hyperpigmented plaques), a dyschromic form (white angular coalescent papules on the neck and dorsa of the hands), and a pigmented melasma-like form (dark patches on the face and neck). There is no mucosal or nail involvement. Histology is characterized by more marked melanin incontinence than in classical lichen planus; there may also be a lighter inflammatory cell infiltrate and focal areas of parakeratosis.
Etiology
Etiology is unknown.
Additional information