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Odontomatosis-aortae esophagus stenosis syndrome

Disease definition

Odontoma-dysphagia syndrome is a malformation syndrome, characterized by odontomas (undifferentiated mass of the esophagus) and severe dysphagia.


  • Synonym(s):
    • Boder syndrome
  • Prevalence: <1 / 1 000 000
  • Inheritance: -
  • Age of onset: No data available
  • ICD-10: -
  • OMIM: 164330
  • UMLS: C1834013
  • MeSH: -
  • GARD: 238
  • MedDRA: -

Additional information

Specialised Social Services

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