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Papilloma of choroid plexus

Disease definition

A rare benign type of choroid plexus tumor often occurring in the fourth ventricle (in adults) and the lateral ventricle (in children) but sometimes arising ectopically in the brain parenchyma, and presenting with nausea, vomiting, papilledema, abnormal eye movements, as well as enlarged head circumference, seizures and gait impairment due to an increase in intracranial pressure.


Classification level: Disorder
  • Synonym(s):
    • CPP
    • Choroid plexus papilloma
  • Prevalence: -
  • Inheritance: -
  • Age of onset: All ages
  • ICD-10: D33.0
  • OMIM: 260500
  • UMLS: C0205770
  • MeSH: D020288
  • GARD: 4214
  • MedDRA: 10008777

Detailed information


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