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Reversible cerebral vasoconstriction syndrome

Disease definition

A rare cerebrovascular disorder characterized by severe headaches with or without focal neurological deficits or seizures, and a reversible segmental and multifocal vasoconstriction of cerebral arteries. It may occur spontaneously or be provoked by various precipitating factors, the most common being postpartum and exposure to various vasoactive substances such as illicit drugs and selective serotonin-reuptake inhibitors. The major complication is ischemic or hemorrhagic stroke.

ORPHA:284388

Classification level: Disorder
  • Synonym(s):
    • RCVS
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: I67.8
  • ICD-11: 8B22.2
  • OMIM: -
  • UMLS: C3544214
  • MeSH: -
  • GARD: 12768
  • MedDRA: -

  A summary on this disease is available in Deutsch (2015) Español (2015) Italiano (2015) Nederlands (2015)

Detailed information

Disease review articles

ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.