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Neuralgic amyotrophy

Disease definition

A rare disorder of the peripheral nervous system characterized by the sudden onset of extreme pain in the upper extremity followed by rapid multifocal motor weakness and atrophy and a slow recovery in months to years. NA includes both an idiopathic (INA, also known as Parsonage-Turner syndrome) and hereditary (HNA) form.


Classification level: Disorder
  • Synonym(s):
    • Acute brachial plexus neuritis
    • Brachial plexus neuritis
    • Immune brachial plexus neuropathy
    • Mononeuritis multiplex with brachial predilection
    • Neuralgic shoulder amyotrophy
  • Prevalence: 1-5 / 10 000
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: Adult
  • ICD-10: G54.5
  • ICD-11: 8B91.0
  • OMIM: 162100
  • UMLS: C1510479
  • MeSH: D020968
  • GARD: 4228
  • MedDRA: 10063020

Detailed information

General public

Genetic Testing

ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)
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