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Idiopathic chronic eosinophilic pneumonia

Disease definition

A rare, severe, interstitial lung disease characterized by insidious onset with subacute or chronic non-specific respiratory manifestations (dyspnea, cough, wheezing) often associated with systemic manifestations (fatigue, malaise, weight loss) and a history of asthma (up to half of patients). Eosinophilia is present in most cases, usually in excess of 1000 cells/mm3.


Classification level: Disorder
  • Synonym(s):
    • Chronic eosinophilic pneumonia
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: J82
  • ICD-11: CB02.11
  • OMIM: -
  • UMLS: C0008680  C2930941
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

Article for general public


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