x

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.

Attention

Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Captcha image

Primary cutaneous anaplastic large cell lymphoma

Disease definition

Primary cutaneous anaplastic large cell lymphoma (C-ALCL) is a rare T-cell non-Hodgkin lymphoma that affects the skin and generally shows no extracutaneous involvement at presentation. It belongs to the spectrum of primary cutaneous CD30+ lymphoproliferative disorders along with lymphomatoid papulosis (see this term) with which it shares overlapping clinical and histopathologic features.

ORPHA:300865

  • Synonym(s):
    • Primary C-ALCL
    • Regressive atypical histiocytosis
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Adult, Childhood, Adolescent
  • ICD-10: C86.6
  • OMIM: -
  • UMLS: C1301362  C1698767
  • MeSH: -
  • GARD: -
  • MedDRA: 10065863

Detailed information

Professionals

Additional information

Further information on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.