Orphanet: Primary cutaneous anaplastic large cell lymphoma

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Primary cutaneous anaplastic large cell lymphoma

Disease definition

Primary cutaneous anaplastic large cell lymphoma (C-ALCL) is a rare T-cell non-Hodgkin lymphoma that affects the skin and generally shows no extracutaneous involvement at presentation. It belongs to the spectrum of primary cutaneous CD30+ lymphoproliferative disorders along with lymphomatoid papulosis (see this term) with which it shares overlapping clinical and histopathologic features.


Classification level: Disorder
  • Synonym(s):
    • Primary C-ALCL
    • Regressive atypical histiocytosis
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Adult, Childhood, Adolescent
  • ICD-10: C86.6
  • OMIM: -
  • UMLS: C1301362  C1698767
  • MeSH: -
  • GARD: -
  • MedDRA: 10065863

Detailed information


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