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Ameloblastic carcinoma

Disease definition

Ameloblastic carcinoma is a rare odontogenic tumor characterized by aggressive clinical course and local destruction, occurring in mandible more often than in maxilla. The most common symptom is a rapidly progressing painful swelling, but it may present as a benign cystic lesion or as a large, rapidly growing mass with ulceration, bone resorption and teeth mobility, as well. The tumor may metastasize, most commonly to the cervical lymph nodes and the lungs.


  • Synonym(s): -
  • Prevalence: <1 / 1 000 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: C41.1
  • OMIM: -
  • UMLS: C1314678
  • MeSH: -
  • GARD: 11855
  • MedDRA: -

Additional information

Further information on this disease

Specialised Social Services

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