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Erythrokeratoderma ''en cocardes''
Disease definition
A rare, genetic, epidermal disorder characterized by intermittent (remitting and recurring), annular, polycyclic, target-like (or 'en cocardes') plaques with concentric rings of scaling erythema occurring on the extremities, flexural areas, and trunk. Concurrent erythrokeratoderma variabilis-like scaly plaques are commonly found in other parts of the body.
ORPHA:315
Classification level: Disorder- Synonym(s):
- Degos genodermatosis "en cocardes"
- Prevalence: <1 / 1 000 000
- Inheritance: Autosomal dominant
- Age of onset: Childhood
- ICD-10: Q82.8
- OMIM: -
- UMLS: -
- MeSH: -
- GARD: 1722
- MedDRA: -
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