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Congenital factor VII deficiency

Disease definition

Factor VII (FVII) deficiency is a rare hereditary hemorrhagic disease caused by the diminution or absence of this coagulation factor.


  • Synonym(s):
    • Congenital proconvertin deficiency
    • Hypoproconvertinemia
  • Prevalence: 1-9 / 1 000 000
  • Inheritance: Autosomal recessive 
  • Age of onset: All ages
  • ICD-10: D68.2
  • OMIM: 227500
  • UMLS: C0015503
  • MeSH: -
  • GARD: 2238
  • MedDRA: 10016079

Detailed information

Article for general public


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