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Goblet cell carcinoma

Disease definition

Goblet cell carcinoma (GCC) is an aggressive type of endocrine tumor of the appendix (see this term) presenting equally in males and females in the fifth decade of life and manifesting with a palpable mass and abdominal pain or acute appendicitis. Metastasis to the ovaries, peritoneum or right colon has usually already occurred in half of patients at the time of diagnosis.


Classification level: Subtype of disorder
  • Synonym(s):
    • GCC
    • Goblet cell adenocarcinoid
    • Goblet cell carcinoid
    • Goblet cell tumor
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C18.1
  • ICD-11: XH7GY6
  • OMIM: -
  • UMLS: C0205695
  • MeSH: -
  • GARD: 10414
  • MedDRA: -

Detailed information


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