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Wild type ATTR amyloidosis

Disease definition

A common form of systemic amyloidosis characterized by deposition of wild type transthyretin predominantly in the heart and the soft tissues (mainly the carpal tunnel region, lumbar canal and tendons).

ORPHA:330001

Classification level: Disorder
  • Synonym(s):
    • ATTRwt amyloidosis
    • ATTRwt-related amyloidosis
    • Senile systemic amyloidosis
    • Wild type ATTR-related amyloidosis
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: E85.8
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

General public

Guidelines

ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)
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