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Disease definition

A rare bacterial infectious disease caused by Francisella tularensis and characterized by six major clinical presentations: ulceroglandular, glandular, oropharyngeal, oculoglandular, pneumonic, or typhoidal, depending on the route of infection. Early flu-like symptoms are common to all forms and are accompanied/followed by either a skin inoculation ulcer with localized lymphadenopathy; isolated lymphadenopathy; chronic pharyngitis with cervical lymphadenopathy; conjunctivitis with localized lymphadenopathy; lung involvement; severe systemic disease with neurological symptoms.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: A21.0  A21.1  A21.2  A21.3  A21.7  A21.8  A21.9
  • ICD-11: 1B94  1B94.0  1B94.Y
  • OMIM: -
  • UMLS: C0041351
  • MeSH: D014406
  • GARD: 396
  • MedDRA: 10045146
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