Orphanet: Idiopathic nephrotic syndrome
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Idiopathic nephrotic syndrome

Disease definition

A rare primary glomerular group of diseases characterized by the triad of edema, massive, or nephrotic-range, proteinuria and hypoalbuminemia, for which there is no known cause. Depending on response to treatment, disease is distinguished into steroid-sensitive nephrotic syndrome (SSNS) and steroid-resistant nephrotic syndrome (SRNS), with the latter being further divided, depending on occurrence, into familial or sporadic forms.

ORPHA:357502

Classification level: Group of disorders
  • Synonym(s): -
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: All ages
  • ICD-10: -
  • OMIM: -
  • UMLS: C3496337
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

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