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Central retinal vein occlusion

Disease definition

A rare retinal vasculopathy characterized by impaired venous return from the retinal circulation due to an occlusion occurring within or posterior to the optic nerve head. The clinical presentation is variable and may range from asymptomatic to an abrupt and profound loss of vision. Complications causing visual loss include macular edema, macular ischemia, optic neuropathy, vitreous hemorrhage, tractional retinal detachment, and in more severe cases extensive capillary non-perfusion with a high risk of neovascular glaucoma.


Classification level: Disorder
  • Synonym(s):
    • CRVO
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: H34.8
  • ICD-11: 9B74.1
  • OMIM: -
  • UMLS: C0154841
  • MeSH: -
  • GARD: -
  • MedDRA: 10007972
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