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Primary effusion lymphoma

Disease definition

Primary effusion lymphoma (PEL) is a large B-cell lymphoma located in the body cavities, characterized by pleural, peritoneal, and pericardial fluid lymphomatous effusions and that is always associated with human herpes virus-8 (HHV-8).


Classification level: Disorder
  • Synonym(s):
    • Body cavity-based lymphoma
    • PEL
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Adult
  • ICD-10: C83.8
  • ICD-11: 2A81.9
  • OMIM: -
  • UMLS: C1292753
  • MeSH: D054685
  • GARD: 9247
  • MedDRA: 10065857
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.