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Mirizzi syndrome

Disease definition

A rare biliary tract disease characterized by external compression and subsequent obstruction of an extrahepatic biliary duct by one or more gallstones in the cystic duct or the gallbladder. Patients may present with acute or chronic cholecystitis with right upper abdominal pain, nausea, and vomiting, jaundice, or cholangitis. Cholecystobiliary or -enteric fistulae can arise due to chronic inflammation and ulceration.

ORPHA:521219

Classification level: Disorder
  • Synonym(s):
    • Extrinsic biliary compression syndrome
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Adult, Elderly
  • ICD-10: K80.8
  • ICD-11: DC11.Y
  • OMIM: -
  • UMLS: C0267878
  • MeSH: D057792
  • GARD: -
  • MedDRA: -

  A summary on this disease is available in Deutsch (2020) Español (2020) Français (2020) Nederlands (2020)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.