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MALT lymphoma

Disease definition

MALT (mucosa-associated lymphoid tissue) lymphoma is a rare form of malignant non-Hodgkin lymphoma (see this term) that affects B cells and grows at the expense of lymphoid tissue associated with mucous membranes, but also occurs, more rarely, in lymph nodes.


Classification level: Disorder
  • Synonym(s):
    • Extranodal marginal zone B-cell lymphoma
    • MALToma
    • Mucosa-associated lymphatic tissue lymphoma
    • Mucosa-associated lymphoid tissue lymphoma
  • Prevalence: 1-9 / 100 000
  • Inheritance: Multigenic/multifactorial or Not applicable 
  • Age of onset: Adult
  • ICD-10: C88.4
  • OMIM: 137245
  • UMLS: C1850900
  • MeSH: -
  • GARD: -
  • MedDRA: 10060707
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