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Hepatoportal sclerosis

Disease definition

A form of portosinusoidal vascular disease characterized histologically by varying degrees of phlebosclerosis, primarily involving the small and medium branches of the portal vein with heterogeneous distribution, in the absence of cirrhosis.

ORPHA:64743

Classification level: Subtype of disorder
  • Synonym(s):
    • Obliterative portal venopathy
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: All ages
  • ICD-10: K74.1
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

Disease review articles

ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.