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Immunoglobulin A vasculitis

Disease definition

A rare, small-vessel vasculitis characterized by skin purpura, arthritis, abdominal and/or renal involvement, IgA tissue deposits (arterioles, capillaries, and venules) and circulating IgA immune complexes.


Classification level: Disorder
  • Synonym(s):
    • Anaphylactoid purpura
    • Henoch-Schönlein purpura
    • IgA vasculitis
    • Purpura rheumatica
    • Rheumatoid purpura
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Childhood
  • ICD-10: D69.0
  • OMIM: -
  • UMLS: C0034152  C0086922
  • MeSH: -
  • GARD: 8204
  • MedDRA: -
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