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Atrophoderma vermiculata

Disease definition

A rare genetic skin disease characterized by childhood onset of follicular keratotic papules slowly progressing to characteristic ''honeycomb'' atrophy on the cheeks, preauricular area, and forehead. Less frequently, the condition may affect also the upper lip, ears, or limbs. Additional features include facial erythema, milia, and follicular plugs.


Classification level: Disorder
  • Synonym(s):
    • Folliculitis ulerythematosa reticulate
  • Prevalence: Unknown
  • Inheritance: Unknown or Autosomal recessive 
  • Age of onset: Childhood
  • ICD-10: L66.4
  • ICD-11: ED56
  • OMIM: 209700  604093
  • UMLS: C0263429
  • MeSH: -
  • GARD: 9744
  • MedDRA: -
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