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Pemphigus erythematosus

Disease definition

A rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed.

ORPHA:79480

Classification level: Disorder
  • Synonym(s):
    • Seborrheic pemphigus
    • Senear-Usher syndrome
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: L10.4
  • OMIM: -
  • UMLS: C0263312
  • MeSH: -
  • GARD: -
  • MedDRA: 10058917

Detailed information

Professionals

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.