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Localized lichen myxedematosus

Disease definition

A group of skin diseases characterized by the development of papules, nodules and/or plaques with mucin deposits and a variable degree of fibrosis in the absence of thyroid disease. The group comprises five sub-forms: nodular lichen myxedematosus, discrete papular lichen myxedematosus, papular mucinosis of infancy, acral persistent papular mucinosis and self-healing papular mucinosis.


Classification level: Group of disorders
  • Synonym(s):
    • Papular mucinosis
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: -
  • ICD-11: EB90.11
  • OMIM: -
  • UMLS: C0263390
  • MeSH: -
  • GARD: 7321
  • MedDRA: -
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