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Plasmacytoma

Disease definition

Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations.

ORPHA:86855

Classification level: Disorder
  • Synonym(s):
    • Solitary plasmacytoma
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C90.2  C90.3
  • OMIM: -
  • UMLS: C0032131
  • MeSH: D010954
  • GARD: -
  • MedDRA: 10035484
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