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Shiga toxin-associated hemolytic uremic syndrome
Disease definition
A rare thrombotic microangiopathy characterized by mechanical hemolytic anemia, thrombocytopenia, and renal dysfunction that is usually associated with prodromal enteritis caused by Shigella dysentriae type 1 or E. Coli.
ORPHA:90038
Classification level: Subtype of disorder- Synonym(s):
- D+ HUS
- EHEC-HUS
- Hemolytic uremic syndrome associated with Shiga toxin-producing Escherichia coli
- Hemolytic uremic syndrome with diarrhea
- STEC-HUS
- Shiga-like toxin-associated HUS
- Stx-HUS
- Typical HUS
- Typical hemolytic uremic syndrome
- Prevalence: Unknown
- Inheritance: Not applicable
- Age of onset: All ages
- ICD-10: D58.8
- OMIM: 235400
- UMLS: -
- MeSH: -
- GARD: -
- MedDRA: -
A summary on this disease is available in Español (2016) Italiano (2016) Nederlands (2016) Polski ()
Detailed information
General public
- Article for general public
- Français (2015) - Minist Santé et Prévention
Guidelines
- Emergency guidelines
- Français (2021, pdf) - Orphanet Urgences
- Clinical practice guidelines
- Deutsch (2016) - AWMF
Disease review articles
- Review article
- English (2012) - Nephrol Dial Transplant


Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.