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Shiga toxin-associated hemolytic uremic syndrome

Disease definition

A rare thrombotic microangiopathy characterized by mechanical hemolytic anemia, thrombocytopenia, and renal dysfunction that is usually associated with prodromal enteritis caused by Shigella dysentriae type 1 or E. Coli.

ORPHA:90038

Classification level: Subtype of disorder
  • Synonym(s):
    • D+ HUS
    • EHEC-HUS
    • Hemolytic uremic syndrome associated with Shiga toxin-producing Escherichia coli
    • Hemolytic uremic syndrome with diarrhea
    • STEC-HUS
    • Shiga-like toxin-associated HUS
    • Stx-HUS
    • Typical HUS
    • Typical hemolytic uremic syndrome
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: D58.8
  • ICD-11: 3A21.Y  XN108
  • OMIM: 235400
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

  A summary on this disease is available in Español (2016) Italiano (2016) Nederlands (2016) Polski ()

Detailed information

General public

Guidelines

Disease review articles

ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.