Search for a rare disease
Other search option(s)
Immunotactoid or fibrillary glomerulopathy
Disease definition
Immunotactoid or fibrillary glomerulopathy is a group of very rare glomerular diseases, composed of immunotactoid glomerulopathy (ITG) and non-amyloid fibrillary glomerulopathy (non-amyloid FGP) (see these terms), that are characterized by mesangial deposition of monoclonal microtubular or polyclonal fibrillar deposits. Both present clinically with nephrotic range proteinuria, hematuria and renal insufficiency leading to renal failure in many cases. ITG is more likely to manifest with underlying lymphoproliferative disease, hypocomplementemia, dysproteinemia, monoclonal gammopathy or occult cryoglobulinemia. Non-amyloid FGP is 10 times more frequent than ITG.
ORPHA:91137
Classification level: Group of disorders- Synonym(s):
- Immunotactoid or fibrillary glomerulonephritis
- Prevalence: <1 / 1 000 000
- Inheritance: Not applicable
- Age of onset: Adult
- ICD-10: -
- OMIM: -
- UMLS: -
- MeSH: -
- GARD: 12741
- MedDRA: -
A summary on this disease is available in Deutsch (2016) Español (2016) Italiano (2016) Nederlands (2016) Français (2008) Português (2008) Polski (2015, pdf) Polski (2015)
Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.