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Renal hypoplasia

Disease definition

A congenital renal malformation characterized by abnormally small kidney(s) (kidney volume below two standard deviations of that of age-matched normal individuals or a combined kidney volume of less than half of what is normal for the patient's age) with normal corticomedullary differentiation and reduced number of nephrons.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: Unknown
  • Inheritance: Not applicable or Autosomal dominant 
  • Age of onset: All ages
  • ICD-10: Q60.3  Q60.4  Q60.5
  • ICD-11: LB30.0Y
  • OMIM: -
  • UMLS: C0266295
  • MeSH: -
  • GARD: -
  • MedDRA: 10049102
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