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VIPoma

Disease definition

VIPoma is an extremely rare type of pancreatic neuroendocrine tumor (see this term) that secretes vasoactive intestinal polypeptide (VIP) leading to the manifestations of watery diarrhea, hypokalemia and achlorhydia or hypochhlorhydia (known as WDHA syndrome).

ORPHA:97282

Classification level: Disorder
  • Synonym(s):
    • Diarrheogenic islet cell tumor
    • Pancreatic cholera
    • VIP-secreting tumor
    • Verner-Morrison syndrome
    • WDHA syndrome
    • Watery diarrhea-hypokalemia-achlorhydria syndrome
  • Prevalence: <1 / 1 000 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: E16.8
  • OMIM: -
  • UMLS: C0011993  C0086768
  • MeSH: D003969
  • GARD: 3787  5493
  • MedDRA: 10047430

Detailed information

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