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Non-amyloid fibrillary glomerulopathy

Disease definition

Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy (ITG, see this term) are often grouped together as pathogenetically related diseases.

ORPHA:97566

Classification level: Disorder
  • Synonym(s):
    • Congo red-negative amyloidosis-like glomerulopathy
    • Non-amyloid fibrillary glomerulonephritis
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: N03.6
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 12740
  • MedDRA: -

Detailed information

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