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Indolent systemic mastocytosis

Disease definition

A rare, usually benign, chronic, form of systemic mastocytosis (SM) characterized by an abnormal accumulation of neoplastic mast cells (MCs) mainly in the bone marrow (BM) but also in other organs or tissues such as preferably the skin.

ORPHA:98848

Classification level: Disorder
  • Synonym(s): -
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: D47.0
  • OMIM: -
  • UMLS: C0272203
  • MeSH: -
  • GARD: -
  • MedDRA: 10056452

Detailed information

Professionals

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.