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105 Resultado(s)

Ordenados por

Financiado por un miembro del IRDiRC =

Proyectos de investigación

ALEMANIA

Baden-Württemberg
HEIDELBERG

Yoga in Patients With Fibrosing Interstitial Lung Diseases
Thoraxklinik-Heidelberg gGmbH
Abteilung für Pneumologie und Beatmungsmedizin

ALEMANIA

Bayern
MÜNCHEN

Financiado por un miembro del IRDiRCHCQ4Surfdefect : Hydroxychloroquine (HCQ) in pediatric ILD -DE-
Kinderklinik und Kinderpoliklinik im Dr. von Haunerschen Kinderspital
Christiane Herzog Ambulanz

ALEMANIA

Berlin
BERLIN

Surface electromyography in patients with Acute Respiratory Distress Syndrome (ARDS)
Charité - Universitätsmedizin Berlin (CBF)
Klinik für Anästhesiologie mit Schwerpunkt operative Intensivmedizin

AUSTRIA

WIEN
WIEN

ALARM: Advisory Lead ARDS Respirator Management
Allgemeines Krankenhaus der Stadt Wien
Klinische Abteilung für Allgemeine Anästhesie und Intensivmedizin

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCInhaled gm-csf therapy of autoimmune pulmonary alveolar proteinosis
Institution: Information not provided - US

FRANCIA

AUVERGNE-RHONE-ALPES
ADDRESS: NOT PROVIDED - FR

FRANCIA

AUVERGNE-RHONE-ALPES
BRON

Genetic transmission of familial forms of sarcoidosis
CHU de Lyon HCL - GH Est
Unité Médicale de Génétique des Cancers et des Maladies Multifactorielles

FRANCIA

AUVERGNE-RHONE-ALPES
BRON

Genetic transmission of familial forms of sarcoidosis
CHU de Lyon HCL - GH Est-Hôpital Louis Pradel
Service de pneumologie

HUNGRIA

Dél-Dunántúl
PECS

IRLANDA

County Galway
GALWAY

Development of a nebulised cell based therapy for acute respiratory distress syndrome
National University of Ireland Galway
School of Medicine

PAISES BAJOS (LOS)

Utrecht
NIEUWEGEIN

Genetic predisposition to interstitital lung diseases and disease phenotypes
St. Antonius Ziekenhuis, locatie Nieuwegein
Longcentrum

ALEMANIA

Berlin
ADDRESS: NOT PROVIDED - DE

Financiado por un miembro del IRDiRCICON: Analysis of uveitism manifestation and outcome
Institution: Information not provided - DE

ALEMANIA

Berlin
BERLIN

JuMBO: Juvenile Arthritis - Methotrexate / Biologics long-term Observation
Deutsches Rheuma-Forschungszentrum Berlin
Forschungsbereich Epidemiologie

ALEMANIA

Nordrhein-Westfalen
MÜNSTER

Financiado por un miembro del IRDiRCICON: Biosample collection and biomarker analysis
Universitätsklinikum Münster
Klinik für Kinder- und Jugendmedizin - Pädiatrische Rheumatologie und Immunologie

ALEMANIA

Nordrhein-Westfalen
SANKT AUGUSTIN

AUSTRIA

TIROL
INNSBRUCK

AUSTRIA

TIROL
INNSBRUCK

Financiado por un miembro del IRDiRCPersTIgAN: Personalized Treatment in IgA Nephropathy - AT
Medizinische Universität Innsbruck
Universitätsklinik für Innere Medizin IV - Nephrologie und Hypertensiologie

CANADA

Ontario
KINGSTON

Financiado por un miembro del IRDiRCIIH-ECC: Idiopathic Infantile Hypercalcemia - European-Canadian Consortium - CA
Queen's University
Department of Biomedical and Molecular Sciences

CANADA

Ontario
TORONTO

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCJuvenile myositis
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCNeuro-ophthalmic mechanisms of disease
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCTargeting jak3 in the treatment of autoimmune disease
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCAcid sphingomyelinase and niemann-pick disease
Institution: Information not provided - US

FRANCIA

AUVERGNE-RHONE-ALPES
GRENOBLE

USIDNET: modelization of X+CGD chronic granulomatous disease and Nox2 super oxidase mutants in the PLB-985 cell line to study the NADPH oxidase activation process
CHU de Grenoble et des Alpes - Institut de biologie et de pathologie
Centre Diagnostic et Recherche sur la Granulomatose Septique Chronique

FRANCIA

AUVERGNE-RHONE-ALPES
LA TRONCHE

NOX NADPH oxydases in inflammatory response: physiopathological aspects, regulation mechanism and modeling
Université Grenoble Alpes (UGA) - Campus santé
GREPI : Groupe de Recherche et d'Etudes du Processus Inflammatoire

FRANCIA

AUVERGNE-RHONE-ALPES
LA TRONCHE

Validation of a new concept of cell therapy by transfer of proteins in enzymopathies: application to the Chronic septic granulomatosis
Université Grenoble Alpes (UGA) - Campus santé
GREPI : Groupe de Recherche et d'Etudes du Processus Inflammatoire

FRANCIA

CENTRE-VAL DE LOIRE
TOURS

Financiado por un miembro del IRDiRCAcoustic Waves and Helium/oxygen for Aerosol Treatment of Idiopathic Pulmonary Fibrosis (IPF)
Faculté de Médecine, Université de Tours François Rabelais
Équipe Inserm 3 : « Aérosolthérapie et biothérapies à visée respiratoire »

FRANCIA

GRAND-EST
STRASBOURG CEDEX

Financiado por un miembro del IRDiRCRare Invisible Disease and Schooling of Children
ESPE de Strasbourg
Equipe Apprentissages, pratiques d'enseignement et d'éducation

FRANCIA

ILE-DE-FRANCE
CRÉTEIL

Surfactant deficiencies in chronic lung diseases in children
Centre Hospitalier Intercommunal de Créteil
Service de pédiatrie - Hôpital de jour

FRANCIA

ILE-DE-FRANCE
PARIS

ERADAS and ERAFI: development and validation of the scores of activity and functional impairment in juvenile spondylitis
Hôpital Necker-Enfants Malades
Développement normal et pathologique du système immunitaire

FRANCIA

ILE-DE-FRANCE
VILLEJUIF

Financiado por un miembro del IRDiRCTransition Platforms: Understanding the Expectations of Parents of Young People with Rare Diseases
CLCC Institut Gustave Roussy
Equipe Epidémiologie des radiations, épidémiologie clinique des cancers et survie

IRLANDA

County Dublin
DUBLIN

IRLANDA

County Dublin
DUBLIN

Urinary sCD163 as a biomarker in crescentic glomerulonephritis
Trinity College Dublin
Trinity Translational Medicine Institute

IRLANDA

County Galway
GALWAY

ITALIA

LOMBARDIA
MILANO

Pathogenesis and therapy of chronic granulomatous disease by gene transfer into hematopoietic stem cells
Istituto San Raffaele Telethon per la Terapia Genica - TIGET
Unità di Ricerca Clinica

ITALIA

LOMBARDIA
MONZA

Nutritional Assessment in Idiopathic Pulmonary Fibrosis: a Pilot Study
Azienda Ospedaliera San Gerardo
Dipartimento Cardio-Toraco-Vascolare

JAPON

JAPAN
KYOTO

Financiado por un miembro del IRDiRCDiscovery of novel therapeutic approach for Nakajo-Nishimura syndrome and Blau syndrome
Center for iPS Cell Research and Application, Kyoto University
Department of Clinical Application

REINO UNIDO (EL)

Greater London
LONDON

SUECIA

Stockholms läns landsting
STOCKHOLM

AUSTRIA

WIEN
WIEN

Financiado por un miembro del IRDiRCRELENT: RELapses prevENTion in chronic autoimmune disease: common mechanisms and co-morbidities - AT
Medizinische Universität Wien
Klinisches Institut für Pathologie

AUSTRIA

WIEN
WIEN

From AAV (ANCA-associated vasculitis) to chronic kidney disease - contribution of TenascinC
Medizinische Universität Wien
Klinisches Institut für Pathologie

AUSTRIA

WIEN
WIEN

Financiado por un miembro del IRDiRCExtracellular Vesicles (EV) as markers of active disease in AAV (ANCA-associated vasculitis) - AT
Medizinische Universität Wien
Klinisches Institut für Pathologie

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCTherapeutics for rare and neglected diseases - science
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCDevelopment of neurosteroids for lysosomal storage disorders
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCGenetic analysis of complex inflammatory disorders
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCGenetic and genomic analysis of niemann pick type c1 disease
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCNovel regulators of inflammatory arthritis and bone erosion
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCPathogenesis of behcet's disease and still's disease
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCClinical investigations of niemann-pick disease; type c
Institution: Information not provided - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

Financiado por un miembro del IRDiRCInborn errors of cholesterol synthesis
Institution: Information not provided - US

IRLANDA

County Dublin
DUBLIN

AVERT: Autoimmunity Relapse Prediction Using Multiple Parallel Data Sources
Trinity College Dublin
Trinity Translational Medicine Institute

ITALIA

FRIULI VENEZIA GIULIA
UDINE

Role of protein misfolding in the pathogenesis of Niemann-Pick type C disease: a possible therapeutic target
Azienda Ospedaliero-Universitaria "Santa Maria della Misericordia" di Udine
Centro di Coordinamento Regionale per le Malattie Rare

ITALIA

FRIULI VENEZIA GIULIA
UDINE

Screening of Niemann Pick type C among patients affected with psychiatric disease of unknown ethiology
Azienda Ospedaliero-Universitaria "Santa Maria della Misericordia" di Udine
Centro di Coordinamento Regionale per le Malattie Rare

ITALIA

PUGLIA
BARI

Physiopathology of HCV-related Cryoglobulinemic Vasculitis: molecular, immunological and clinical analisys
Azienda Ospedaliero-Universitaria Consorziale Policlinico di Bari
Unità di Epatologia - Sezione di Medicina Interna e Oncologia Clinica

ITALIA

TOSCANA
PISA

Study of cellular mechanisms of neuronal dysfunction in Niemann Pick type C disease and identification of neuroprotective therapies
Fondazione "Gabriele Monasterio" - Consiglio Nazionale delle Ricerche CNR
Area della Ricerca

JAPON

JAPAN
CHIBA

Financiado por un miembro del IRDiRCPathological analysis and development ofan innovative therapeutic agent ofniemann-pick disease type C
Graduate School of Pharmaceutical Sciences, Chiba University
Laboratory of Chemical Pharmacology

JAPON

JAPAN
KUMAMOTO

Financiado por un miembro del IRDiRCDeveloping new drugs for Niemann-Pick disease type C
Institute of Molecular Embryology and Genetics, Kumamoto University
Department of Cell Modulation

JAPON

JAPAN
OSAKA

Financiado por un miembro del IRDiRCDeveloping the disease specific therapy for ANCA-associated vasculitis focused on immune regulatory factors in neutrophils
Osaka University Graduate School of Medicine
Department of Respiratory Medicine and Clinical Immunology

PORTUGAL

NORTE
PORTO

The sorting and trafficking of lysosomal proteins through M6P independent pathways: molecular, biochemical and functional studies
Instituto Nacional de Saúde Dr. Ricardo Jorge - Porto
Unidade de Investigação & Desenvolvimento; Departamento de Genética

REINO UNIDO (EL)

Glasgow
GLASGOW

Financiado por un miembro del IRDiRCHarnessing the power of integrated data to investigate environmental exposures on ANCA vasculitis risk , an unbiased approach -GB
Institute of Infection, Immunity and Inflammation, University of Glasgow
Institute of Infection, Immunity and Inflammation

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

ESTADOS UNIDOS

Washington
ADDRESS: NOT PROVIDED - US

FRANCIA

ILE-DE-FRANCE
PARIS

Model contribution in the microeconomic assessment of therapeutic strategies in Wegener granulomatosis
CHU Paris Centre - Hôpital Cochin, Site Cochin
Service de Santé publique : Gestion des risques et qualité

Proyectos de investigación multicéntricos