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Acute interstitial pneumonia

Disease definition

A rare rapidly progressive and histologically distinct form of idiopathic interstitial pneumonia.


Classification level: Disorder
  • Synonym(s):
    • Acute interstitial pneumonitis
    • Hamman-Rich syndrome
  • Prevalence: 1-9 / 100 000
  • Inheritance: Unknown 
  • Age of onset: Adult
  • ICD-10: J84.1
  • OMIM: 178500
  • UMLS: C0085786  C1279945
  • MeSH: -
  • GARD: 12835
  • MedDRA: 10066728
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