Orphanet: Primaire erytromelalgie

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Primary erythromelalgia

Disease definition

Primary erythermalgia is characterized by intermittent attacks of red, warm, painful burning extremities. It spontaneously arises during early childhood and adolescence in the absence of any detectable underlying disorder.


Classification level: Disorder
  • Synonym(s):
    • Primary erythermalgia
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant 
  • Age of onset: All ages
  • ICD-10: I73.8
  • OMIM: 133020
  • UMLS: C0014805
  • MeSH: -
  • GARD: 6377
  • MedDRA: -

Detailed information


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