Orphanet: Behavioral variant of frontotemporal dementia

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Behavioral variant of frontotemporal dementia

Disease definition

Behavioral variant of frontotemporal dementia (bv-FTD) is a form of frontotemporal dementia (FTD; see this term), characterized by progressive behavioral impairment and a decline in executive function with frontal lobe-predominant atrophy.


Classification level: Disorder
  • Synonym(s):
    • bv-FTD
  • Prevalence: -
  • Inheritance: Autosomal dominant 
  • Age of onset: Adult
  • ICD-10: G31.0
  • OMIM: 172700  600274  600795  616437
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

Article for general public


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