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True unicornuate uterus

Disease definition

True unicornuate uterus is a rare, non-syndromic uterovaginal malformation characterized by a crescent-shaped, small-sized uterus containing a single horn and fallopian tube with no rudimentary horn. Urinary tract anomalies are frequently associated.


  • Synonym(s):
    • Complete unilateral Müllerian aplasia
    • Complete unilateral aplasia of the Müllerian ducts
    • Unicornuate uterus without rudimentary horn
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: Q51.4
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -

Additional information

Further information on this disease

Specialised Social Services

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