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Autoimmune hepatitis

Disease definition

Chronic autoimmune hepatitis (AIH) is a rare progressive inflammatory disorder of unknown cause primarily affecting women and associated with circulating autoantibodies, elevated transaminase levels, and increased levels of immunoglobulin.


Classification level: Disorder
  • Synonym(s):
    • Chronic autoimmune hepatitis
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: K75.4
  • OMIM: -
  • UMLS: C0241910
  • MeSH: -
  • GARD: 5871
  • MedDRA: 10003827

Detailed information


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