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IgG4-related mesenteritis

Disease definition

Sclerosing mesenteritis (SM) is a rare pathological disease causing inflammation of the adipose tissue of the small bowel mesentery and is commonly associated with abdominal pain, diarrhea, nausea, weight loss, bloating and loss of appetite. The two subforms include mesenteric panniculitis (where inflammation and fatty necrosis are dominant features) and retractile mesenteritis (where fibrosis and retraction dominate).

ORPHA:238593

Classification level: Subtype of disorder
  • Synonym(s):
    • Isolated mesenteric lipodystrophy
    • Lipomatous mesenteritis
    • Liposclerotic mesenteritis
    • Mesenteric lipogranuloma
    • Mesenteric panniculitis
    • Sclerosing mesenteritis
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: K65.8
  • OMIM: -
  • UMLS: C0025470  C0267770
  • MeSH: -
  • GARD: 8169
  • MedDRA: -

Detailed information

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The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.