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Centrifugal lipodystrophy

Disease definition

Centrifugal lipodystrophy is a rare, acquired, localized lipodistrophy characterized by single or, occasionally, multiple, centrifugally progressive, asymptomatic to sometimes mildly tender, hypopigmented, lipoatrophic skin depressions with weakly erymatheous inflammatory borders, typically associated with regional ipsilateral lymph nodes swelling. Lesions typically occur on lower trunk (in particular groin and abdomen region), followed by upper trunk (axilla and neighboring regions) and, rarely, neck and head. It is usually not associated with systemic disease and is typically self-resolving.

ORPHA:90156

Classification level: Disorder
  • Synonym(s):
    • Lipodystrophia centrifugalis abdominalis infantilis
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: E88.1
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: -
  • MedDRA: -
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