Adenocarcinoma of the liver and intrahepatic biliary tract
A rare hepatic and biliary tract tumor characterized by a growth pattern ressembling that found in hepatocellular carcinomas and cholangiocarcinomas but presenting atypical histological and immunohistochemical features (such as trabecular, organoid, microcystic and/or blastemal-like architecture and inhibin A, cytokeratin 7 and/or cytokeratin 19 positivity) that do not allow a formal diagnosis of the more common aforementioned liver cancers. Patients may present abdominal distension and pain, a palpable abdominal mass and elevated liver enzymes.
- Adenocarcinoma of the liver and IBT
Inheritance: Not applicable
Age of onset: Adult
: produced/endorsed by ERN(s) : produced/endorsed by FSMR(s)
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